Unilateral aplasia of the middle cranial fossa floor in atypical hemifacial microsomia.
نویسندگان
چکیده
We present the first report of a patient with atypical hemifacial microsomia (HFM) and unilateral aplasia of the floor of the middle cranial fossa, glenoid fossa, and portions of her posterior fossa. The patient also developed a Chiari I malformation with cervical syrinx over a 3-year interval. This case report highlights the critical role of imaging in revealing serious, but clinically occult, structural abnormalities, as well as the evolution in the pathogenetic understanding of HFM.
منابع مشابه
Hemifacial microsomia: a clinicoradiographic report of a case
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ورودعنوان ژورنال:
- AJNR. American journal of neuroradiology
دوره 22 7 شماره
صفحات -
تاریخ انتشار 2001